Caso clínico: hemangioendotelioma epitelioide orbitario / Case report: Orbital epithelioid haemangioendothelioma

CASO CLÍNICO: Paciente masculino de 13 años de edad, el cual presenta proptosis y desplazamiento lateral de ojo derecho. Se palpa tumoración blanda no pulsátil en región orbitaria superomedial. Se realizó biopsia excisional de la masa que fue informada como hemangioendotelioma epitelioide. DISCUSIÓN: El hemangioendotelioma epitelioide es un tumor vascular de comportamiento intermedio entre tumores vasculares malignos y benignos. Estos pueden presentarse en tejidos blandos o a partir de hueso. En la literatura hay pocos casos publicados de aparición en órbita

CASE REPORT: A 13-year-old boy presented with right eye proptosis and lateral dystopia. A soft non-pulsatile mass was found in the superomedial orbital region. An excisional biopsy was performed, for which the histopathology reported an epithelioid haemangioendothelioma. DISCUSSION: Haemangioendothelioma is a borderline vascular lesion within the spectrum of clinically benign and malignant tumours. These can arise from soft tissue or bone. There are few reports of these tumours located in the orbit

Liposarcoma de la órbita / Orbital liposarcoma

CASO CLÍNICO:Varón de 46 años de edad que se presenta con proptosis derecha de 18 meses de evolución e hiperemia conjuntival. Se muestra en tomografía una masa intraconal bien delimitada, y en resonancia magnética la masa es hipointensa en T1 que refuerza con gadolinio e hiperintensa en T2. Se realiza biopsia escisional y el resultado de la histopatología fue de liposarcoma bien diferenciado. DISCUSIÓN: El liposarcoma es un tumor maligno del tejido adiposo, muy raro en órbita, con 5 variantes histológicas, más común la mixoide. El tratamiento de elección es escisión quirúrgica amplia y se puede acompañar con radioterapia. Presenta una tasa de recurrencia elevada por tratarse de un tumor infiltrativo

CASER REPORT: The case is presented of a 46-year-old male with right eye proptosis and conjunctival hyperaemia, of 18 months onset. A well-defined intraconal mass was found in the computed tomography. In magnetic resonance this was hypo-intense on T1, enhanced with gadolinium and hyperintense on T2. Excisional biopsy was performed, which was reported as a well-differentiated liposarcoma in the histopathology study. DISCUSSION: Liposarcoma is a malignant adipose tissue tumour. It is very rare in the orbit, with 5 histological types, the most common being myxoid. The treatment of choice is wide surgical excision and may be accompanied with radiotherapy. As it is an infiltrative tumour, It has a high rate of recurrence

Orbital liposarcoma. / Liposarcoma de la órbita.

CASE REPORT: The case is presented of a 46-year-old male with right eye proptosis and conjunctival hyperaemia, of 18 months onset. A well-defined intraconal mass was found in the computed tomography. In magnetic resonance this was hypo-intense on T1, enhanced with gadolinium and hyperintense on T2. Excisional biopsy was performed, which was reported as a well-differentiated liposarcoma in the histopathology study. DISCUSSION: Liposarcoma is a malignant adipose tissue tumour. It is very rare in the orbit, with 5 histological types, the most common being myxoid. The treatment of choice is wide surgical excision and may be accompanied with radiotherapy. As it is an infiltrative tumour, It has a high rate of recurrence.

Case report: Orbital epithelioid haemangioendothelioma. / Caso clínico: hemangioendotelioma epitelioide orbitario.

CASE REPORT: A 13-year-old boy presented with right eye proptosis and lateral dystopia. A soft non-pulsatile mass was found in the superomedial orbital region. An excisional biopsy was performed, for which the histopathology reported an epithelioid haemangioendothelioma. DISCUSSION: Haemangioendothelioma is a borderline vascular lesion within the spectrum of clinically benign and malignant tumours. These can arise from soft tissue or bone. There are few reports of these tumours located in the orbit.