Assuntos
Lipossarcoma Mixoide/diagnóstico , Mixoma/diagnóstico , Neoplasias Vulvares/diagnóstico , Antineoplásicos/farmacologia , Antineoplásicos/uso terapêutico , Biomarcadores Tumorais/metabolismo , Diagnóstico Diferencial , Feminino , Hormônio Liberador de Gonadotropina/agonistas , Humanos , Lipossarcoma Mixoide/patologia , Lipossarcoma Mixoide/fisiopatologia , Lipossarcoma Mixoide/cirurgia , Pessoa de Meia-Idade , Mixoma/patologia , Mixoma/fisiopatologia , Mixoma/cirurgia , Receptores de Estrogênio/metabolismo , Receptores de Progesterona/metabolismo , Neoplasias Vulvares/patologia , Neoplasias Vulvares/fisiopatologia , Neoplasias Vulvares/cirurgiaRESUMO
Malignant tumours of the heart and pericardium are rare. Secondary tumours are 20 to 40 times more common than primary tumours. The authors report the case of a cardiac metastasis of a myxoid liposarcoma of the inguinal region. Surgical ablation with chemotherapy significantly improved the patient' clinical and haemodynamic status. A review of the literature shows that postoperative survival does not exceed 2 years, but the prognosis is better when chemotherapy is associated with surgery. Transoesophageal echocardiography is an excellent diagnostic imaging method. It provides a better evaluation of the tumour and its location, compared to thoracic CT scan and transthoracic echocardiography.
Assuntos
Neoplasias Abdominais/patologia , Neoplasias Cardíacas/secundário , Lipossarcoma Mixoide/secundário , Adulto , Ecocardiografia Transesofagiana , Virilha , Neoplasias Cardíacas/diagnóstico por imagem , Neoplasias Cardíacas/fisiopatologia , Neoplasias Cardíacas/cirurgia , Humanos , Lipossarcoma Mixoide/diagnóstico por imagem , Lipossarcoma Mixoide/fisiopatologia , Lipossarcoma Mixoide/cirurgia , MasculinoRESUMO
A 12-year-old girl developed a myxoid liposarcoma on the inner side of her right thigh. Liposarcomas are extremely rare at this age compared to benign lipoblastomas, which are the most frequent tumors of fatty tissue in childhood. The prognosis of myxoid liposarcoma is good, especially when, as in this patient, the tumor is located in the subcutis where a large and deep excision is possible and often curative.