Langerhans cell histiocytosis
Clin. transl. oncol. (Print)
; 10(11): 688-696, nov. 2008. ilus, tab
Article
em En
| IBECS
| ID: ibc-123543
Biblioteca responsável:
ES1.1
Localização: BNCS
ABSTRACT
Langerhans cell histiocytosis (LCH) is a poorly understood proliferative disease, with different patterns of clinical presentation. Currently it is classified according to the number and type of system involved and the degree of organ dysfunction. The aetiology of the disease remains uncertain, and in some cases the disease is polyclonal, suggesting a reactive condition. Many cytokines have been implicated in the pathogenesis of LCH. Different therapeutic approaches can be considered depending on the affected organ, including surgery, radiotherapy and chemotherapy. Long-term organ dysfunction may remain, despite disease control and/or eradication, making indefinite supportive treatment mandatory. Here we present a literature review on all of the aspects of the disease, treatment approaches and existing protocols, and finally an adult clinical case (AU)
RESUMEN
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Coleções:
06-national
/
ES
Base de dados:
IBECS
Assunto principal:
Ensaios Clínicos Controlados Aleatórios como Assunto
/
Histiocitose de Células de Langerhans
/
Estudos Multicêntricos como Assunto
Tipo de estudo:
Clinical_trials
/
Guideline
/
Prognostic_studies
Limite:
Adolescent
/
Adult
/
Female
/
Humans
/
Male
Idioma:
En
Revista:
Clin. transl. oncol. (Print)
Ano de publicação:
2008
Tipo de documento:
Article