Fahr’s Syndrome – A Case Report / Síndrome de Fahr: un caso clínico

ABSTRACT

Fahr’s syndrome is an uncommon neurodegenerative disorder, characterized by bilateral and extensive deposition of calcium in the basal ganglia.We present the case of a 66-year-old female presented to the Emergency Department with (a sudden and) intense holocranial headache accompanied by nausea. She also reported paresthesias of the hands and feet with several years of evolution, mnesic changes and periods of uninhibited behavior. Head CT revealed extensive and bilateral calcifications of the basal ganglia, cerebellum and frontal region and the analytical findings showed a severe hypocalcemia. She begun replacement with intravenous and oral calcium. An improvement of signs and symptoms were observed during the hospitalization.Although rare, Fahr’s syndrome must be kept in mind and appropriate treatment should be aplied in order to stop it’s progression and improve the clinic symptoms and signs. (AU)