Masa intraabdominal de difícil diagnóstico: tumor fibroso peritoneal solitario / Intraabdominal mass with difficult diagnosis: Solitary fibrous tumor
Gastroenterol. hepatol. (Ed. impr.)
; 33(4): 303-306, Abr. 2010. tab, ilus
Article
em Es
| IBECS
| ID: ibc-84019
Biblioteca responsável:
ES1.1
Localização: BNCS
RESUMEN
El tumor fibroso solitario es un tumor raro de origen mesenquimal, de localización preferentemente en la pleura y las meninges, y menos frecuentemente se diagnostica como masa asintomática peritoneal hepática, en el páncreas o renal. Los hallazgos clínicos y radiológicos no son específicos, aunque nos permiten sospechar una evolución maligna por invasión o metástasis. Sin embargo, la citología preoperatoria suele ser de resultado dudoso o equívoco. Por tanto, el diagnóstico definitivo se logra tras la resección quirúrgica y el estudio mediante inmunohistoquímica con marcadores tales como CD34, vimentina y desmina. Presentamos un caso de tumor fibroso solitario de difícil diagnóstico, incluso tras una extensa serie de pruebas de imagen (AU)
ABSTRACT
Solitary fibrous tumor (SFT) is a rare neoplasm of mesenchymal origin. The most commonly reported locations are the pleura and meninges. Less frequently, SFT manifests as an asymptomatic mass in the pancreas, liver, peritoneum or kidney. Clinical and radiological findings have failed to provide any specific diagnostic pattern but allow malignant development to be suspected due to infiltration or metastasis. In addition, preoperative cytology often yields inconclusive or misleading results. Therefore the definitive diagnosis is achieved after both surgical resection and immunohistochemical analysis, with markers such as CD34, vimentin and desmin. We present a case of SFT, which was difficult to diagnose, even after an extensive battery of tests based on imaging techniques (AU)
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Coleções:
06-national
/
ES
Base de dados:
IBECS
Assunto principal:
Neoplasias Peritoneais
/
Tumores Fibrosos Solitários
Tipo de estudo:
Diagnostic_studies
Limite:
Humans
/
Male
Idioma:
Es
Revista:
Gastroenterol. hepatol. (Ed. impr.)
Ano de publicação:
2010
Tipo de documento:
Article