[Familial complete atrioventricular block in patients with hypertrophic cardiomyopathy]. / Bloqueio atrioventricular total familiar em pacientes com cardiomiopatia hipertrófica.

ABSTRACT

The association of spontaneous complete heart block and hypertrophic cardiomyopathy is rare. We have studied three patients of the same family, two brothers and one nephew, ages 19-41 years, with hypertrophic cardiomyopathy confirmed by hemodynamic and angiographic studies. All patients were treated with permanent cardiac pacemaker implant. They are asymptomatic, aging 33 to 55 years, with follow-up of 157 to 176 months after the onset of the heart block.