Hyperimmunoglobulin E syndrome with juvenile dermatomyositis and calcinosis.
Clin Rheumatol
; 32 Suppl 1: S51-3, 2013 Mar.
Article
em En
| MEDLINE
| ID: mdl-20373123
ABSTRACT
Juvenile dermatomyositis (JDM) is a rare childhood disease with autoimmune association. Environmental factors are known to trigger JDM in genetically susceptible individuals (Schmieder et al., Dermatol Online 63, 2009). Calcinosis is a well-established complication of JDM. Prevalence is higher in children (30-70%; Özkaya et al., Erciyes Med J 30(1)40-43, 2008). Hyperimmunoglobulin E syndrome is a primary immunodeficiency syndrome with multiple recurrent abscess formation and raised serum immunoglobulin E levels. We report a case of JDM with calcinosis cutis universalis with hyperimmunoglobulin E syndrome. With a previous similar case report (Min et al., Korean J Intern Med 1495-98, 1999), this could well be a new sequence syndrome where abscesses are the trigger for the onset of JDM.
Texto completo:
1
Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Calcinose
/
Imunoglobulina E
/
Dermatomiosite
/
Abscesso
/
Síndrome de Job
Tipo de estudo:
Etiology_studies
/
Risk_factors_studies
Limite:
Child
/
Humans
/
Male
Idioma:
En
Revista:
Clin Rheumatol
Ano de publicação:
2013
Tipo de documento:
Article
País de afiliação:
Índia