Biot's breathing in a woman with fatal familial insomnia: is there a role for noninvasive ventilation?
J Clin Sleep Med
; 7(1): 89-91, 2011 Feb 15.
Article
em En
| MEDLINE
| ID: mdl-21344052
ABSTRACT
We present the case of a 48-year-old woman suffering from fatal familial insomnia (FFI)--a rare prion disease--who developed Biot's breathing and secondary respiratory failure during the early stages of the illness. Once hypercapnia was detected a trial of nocturnal noninvasive ventilation (NIV) was offered with important improvement of arterial blood gases (ABG), and subjective good quality of sleep. To our knowledge, this is the first report in the medical literature of the use of NIV in the management approach of this devastating disease. Its impact on the prognosis and survival of these patients, however, is yet to be elucidated.
Palavras-chave
Texto completo:
1
Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Insuficiência Respiratória
/
Insônia Familiar Fatal
/
Hipercapnia
Tipo de estudo:
Diagnostic_studies
/
Etiology_studies
/
Prognostic_studies
Limite:
Female
/
Humans
/
Middle aged
Idioma:
En
Revista:
J Clin Sleep Med
Ano de publicação:
2011
Tipo de documento:
Article
País de afiliação:
Espanha