[Bloch-Sulzberger's syndrome (Incontinentia pigmenti). Contribution with a case report]. / Síndrome de Bloch-Sulzberger (Incontinentia pigmenti). Características y aporte de un caso clínico.

Incontinentia pigmenti (IP) is a rare genodermatosis. Skin lesions, that are present in all patients affected, evolve in stages. The first is the erythematous blistering stage, wich differential diagnosis includes a wide variety of diseases. We present a case of a female neonate with blisters present at birth, where the skin biopsy confirmed the diagnosis of IP.