Isolated intracranial Rosai Dorfman disease.
Neurol India
; 59(3): 443-6, 2011.
Article
em En
| MEDLINE
| ID: mdl-21743180
ABSTRACT
Rosai Dorfman disease (RDD), also known as sinus histiocytosis with massive lymphadenopathy, is a benign histiocytic proliferative disorder mainly affecting the lymph nodes. Although several cases of extra-nodal involvement have been reported previously, central nervous system involvement, particularly in the absence of nodal disease is extremely rare. We report a case of isolated intracranial RDD occurring in a relatively elder patient, which was shown by histological examination to have a dura-based involvement.
Texto completo:
1
Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Histiocitose Sinusal
/
Doenças do Sistema Nervoso Central
Tipo de estudo:
Etiology_studies
Limite:
Humans
/
Male
/
Middle aged
Idioma:
En
Revista:
Neurol India
Ano de publicação:
2011
Tipo de documento:
Article
País de afiliação:
Índia