Massive splenomegaly and pancytopenia reuealing sarcoidosis in a child.
Sarcoidosis Vasc Diffuse Lung Dis
; 30(2): 149-52, 2013 Aug 01.
Article
em En
| MEDLINE
| ID: mdl-24071888
ABSTRACT
Clinical presentation of sarcoidosis in children is very variable and dependant upon age. Herein, we report the first association of massive splenomegaly and pancytopenia as the revealing mode of sarcoidosis in an 8-year-old girl who, despite bone marrow involvement, had a remarkable good outcome following steroid therapy.
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Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Pancitopenia
/
Esplenomegalia
Limite:
Child
/
Humans
Idioma:
En
Revista:
Sarcoidosis Vasc Diffuse Lung Dis
Assunto da revista:
ALERGIA E IMUNOLOGIA
/
ANGIOLOGIA
Ano de publicação:
2013
Tipo de documento:
Article
País de afiliação:
França