Células Ciliadas Auditivas/patologia; Células Fotorreceptoras/patologia; Síndromes de Usher/genética; Síndromes de Usher/patologia; Animais; Proteínas de Transporte/genética; Proteínas de Transporte/metabolismo; Modelos Animais de Doenças; Células Ciliadas Auditivas/metabolismo; Humanos; Células Fotorreceptoras/metabolismo; Síndromes de Usher/metabolismo

4.1 protein, ezrin, radixin, moesin; AMPA; CD; CDH23; CIB2; Cochlear hair cell; EAR; FERM; GST; LTLD; Mechanotransduction; MyTH4; PCDH15; PDZ; PDZ domain containing 7; PDZD7; Photoreceptor; RP; RPE; RPE65; Retinitis pigmentosa; Ribbon synapse; SNAP25; SNARE; TMHS; USH; UTLD; Usher syndrome; VLGR1; cadherin 23; calcium integrin binging protein 2; cytoplasmic domain; deaf circler; dfcr; epilepsy associated repeat; glutathione S-transferase; lower tip link density; myosin tail homology 4; post synaptic density protein (PSD95), Drosophila disk large tumor suppressor (Dlg1), Zonula occludens-1 protein (zo-1); protocadherin 15; retinal pigment epithelium; retinal pigment epithelium-specific 65kDa protein; soluble NSF attachment protein receptor; synaptosomal-associated protein 25; tetraspan membrane protein of hair cell stereocilia; upper tip link density; very large G-coupled protein receptor type 1; α-amino-3-hydroxy-5-methyl-4-isoxazolepropionic acid