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Early onset of tuberous sclerosis with chylous ascites: a case report.
Dalili, Hosein; Amini, Elahe; Akbari Asbagh, Parvin; Esmaeilnia Shrivany, Tahereh; Niknafs, Nikoo; Nayyeri, Fatemeh; Shariat, Mamak; Talebian, Saharnaz; Akbari Asbagh, Naser; Ghorban Sabagh, Vafa.
Afiliação
  • Dalili H; Family Health Institute, Breastfeeding Research Center, Tehran University of Medical Sciences, Tehran, Iran.
  • Amini E; Family Health Institute, Maternal- Fetal& Neonatal Research Center, Tehran University of Medical Sciences, Tehran, Iran.
  • Akbari Asbagh P; Dept. of Pediatric, School of Medicine, Tehran University of Medical Sciences, Tehran, Iran.
  • Esmaeilnia Shrivany T; Family Health Institute, Breastfeeding Research Center, Tehran University of Medical Sciences, Tehran, Iran.
  • Niknafs N; Family Health Institute, Maternal- Fetal& Neonatal Research Center, Tehran University of Medical Sciences, Tehran, Iran.
  • Nayyeri F; Family Health Institute, Maternal- Fetal& Neonatal Research Center, Tehran University of Medical Sciences, Tehran, Iran.
  • Shariat M; Family Health Institute, Maternal- Fetal& Neonatal Research Center, Tehran University of Medical Sciences, Tehran, Iran.
  • Talebian S; Family Health Institute, Breastfeeding Research Center, Tehran University of Medical Sciences, Tehran, Iran.
  • Akbari Asbagh N; Family Health Institute, Breastfeeding Research Center, Tehran University of Medical Sciences, Tehran, Iran.
  • Ghorban Sabagh V; Family Health Institute, Breastfeeding Research Center, Tehran University of Medical Sciences, Tehran, Iran.
Iran J Public Health ; 44(3): 407-11, 2015 Mar.
Article em En | MEDLINE | ID: mdl-25905086
ABSTRACT

BACKGROUND:

Tuberous Sclerosis Complex (TSC) is an autosomal-dominant hereditary disorder. This syndrome is characterized by tumor-like malformations in several organs, as well as the heart. This report summarizes a case of TSC in a premature infant, born at 34 weeks' gestation with ascites. After birth, multiple cardiac mass, subependymal cysts and hypopigmented macules were detected. To our knowledge, this is the first case report of early onset of TSC with chylous ascites in Iran.
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Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Idioma: En Revista: Iran J Public Health Ano de publicação: 2015 Tipo de documento: Article País de afiliação: Irã

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Idioma: En Revista: Iran J Public Health Ano de publicação: 2015 Tipo de documento: Article País de afiliação: Irã