Globodontia in the Otodental Syndrome: A Rare Defect of Tooth Morphology Occurring with Hearing Loss in an Eight-Year-Old.
Dent Update
; 42(10): 927-30, 932, 2015 Dec.
Article
em En
| MEDLINE
| ID: mdl-26855998
ABSTRACT
Otodental syndrome is a hereditary disorder comprising globodontia and sensorineural hearing loss. Globodontia is characterized by distinctively bulbous, enlarged crowns of molar and primary canine teeth. Anomalies including taurodontism and hypodontia also occur. We report on the dental treatment and multidisciplinary management of an eight-year-old girl with this rare condition. Referral to Clinical Genetics and Oral Pathology was instrumental in establishing a diagnosis of otodental syndrome for this young patient and her mother, who had similar dental defects. CPD/Clinical Relevance To increase awareness among practitioners of this rare dental disorder and highlight the need for multidisciplinary management of such cases.
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Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Anormalidades Dentárias
/
Coloboma
/
Transtornos Cromossômicos
/
Perda Auditiva Neurossensorial
Limite:
Child
/
Female
/
Humans
Idioma:
En
Revista:
Dent Update
Ano de publicação:
2015
Tipo de documento:
Article