Expanding the clinical spectrum of self-limiting, rare Kikuchi disease - A case with overwhelming multi-organ involvement.
Neth J Med
; 75(3): 112-116, 2017 Apr.
Article
em En
| MEDLINE
| ID: mdl-28469047
ABSTRACT
Kikuchi disease is a rare disorder with an unknown pathogenesis and a typically self-limiting natural course in predominantly previously healthy young women. Here we present a 54-year-old woman suffering from an overwhelming presentation of Kikuchi disease, associated with haemophagocytic syndrome, liver cell necrosis and nephrotic syndrome. She recovered fully without immunosuppressive treatment. This case report adds to the already broad clinical spectrum of Kikuchi disease described in literature. Awareness among physicians of the full clinical spectrum of Kikuchi disease and the self-limiting nature of this syndrome leads to a good diagnostic approach and may prevent initiation of longstanding immunosuppressive therapy.
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Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Linfadenite Histiocítica Necrosante
/
Linfo-Histiocitose Hemofagocítica
/
Fígado
/
Insuficiência de Múltiplos Órgãos
/
Síndrome Nefrótica
Tipo de estudo:
Diagnostic_studies
/
Etiology_studies
Limite:
Female
/
Humans
/
Middle aged
Idioma:
En
Revista:
Neth J Med
Ano de publicação:
2017
Tipo de documento:
Article
País de afiliação:
Holanda