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Modulation of oxidative phosphorylation and redox homeostasis in mitochondrial NDUFS4 deficiency via mesenchymal stem cells.
Melcher, Marlen; Danhauser, Katharina; Seibt, Annette; Degistirici, Özer; Baertling, Fabian; Kondadi, Arun Kumar; Reichert, Andreas S; Koopman, Werner J H; Willems, Peter H G M; Rodenburg, Richard J; Mayatepek, Ertan; Meisel, Roland; Distelmaier, Felix.
Afiliação
  • Melcher M; Department of General Pediatrics, Neonatology and Pediatric Cardiology, University Children's Hospital, Heinrich Heine University Düsseldorf, Moorenstraße 5, 40225, Düsseldorf, Germany.
  • Danhauser K; Department of General Pediatrics, Neonatology and Pediatric Cardiology, University Children's Hospital, Heinrich Heine University Düsseldorf, Moorenstraße 5, 40225, Düsseldorf, Germany.
  • Seibt A; Department of General Pediatrics, Neonatology and Pediatric Cardiology, University Children's Hospital, Heinrich Heine University Düsseldorf, Moorenstraße 5, 40225, Düsseldorf, Germany.
  • Degistirici Ö; Division of Pediatric Stem Cell Therapy, Clinic for Pediatric Oncology, Hematology and Clinical Immunology, Medical Faculty, Heinrich Heine University Medical Center, Düsseldorf, Germany.
  • Baertling F; Department of General Pediatrics, Neonatology and Pediatric Cardiology, University Children's Hospital, Heinrich Heine University Düsseldorf, Moorenstraße 5, 40225, Düsseldorf, Germany.
  • Kondadi AK; Institute of Biochemistry and Molecular Biology I, Medical Faculty, Heinrich Heine University, Düsseldorf, Germany.
  • Reichert AS; Institute of Biochemistry and Molecular Biology I, Medical Faculty, Heinrich Heine University, Düsseldorf, Germany.
  • Koopman WJH; Department of Biochemistry (286), Radboud Institute for Molecular Life Sciences, Radboud University Nijmegen (Radboudumc), Nijmegen, The Netherlands.
  • Willems PHGM; Department of Biochemistry (286), Radboud Institute for Molecular Life Sciences, Radboud University Nijmegen (Radboudumc), Nijmegen, The Netherlands.
  • Rodenburg RJ; Radboud Center for Mitochondrial Medicine (RCMM), Department of Pediatrics, 774 Translational Metabolic Laboratory (TML), Radboud University Medical Center, P.O. Box 9101, 6500 HB, Nijmegen, The Netherlands.
  • Mayatepek E; Department of General Pediatrics, Neonatology and Pediatric Cardiology, University Children's Hospital, Heinrich Heine University Düsseldorf, Moorenstraße 5, 40225, Düsseldorf, Germany.
  • Meisel R; Division of Pediatric Stem Cell Therapy, Clinic for Pediatric Oncology, Hematology and Clinical Immunology, Medical Faculty, Heinrich Heine University Medical Center, Düsseldorf, Germany.
  • Distelmaier F; Department of General Pediatrics, Neonatology and Pediatric Cardiology, University Children's Hospital, Heinrich Heine University Düsseldorf, Moorenstraße 5, 40225, Düsseldorf, Germany. Felix.Distelmaier@med.uni-duesseldorf.de.
Stem Cell Res Ther ; 8(1): 150, 2017 06 24.
Article em En | MEDLINE | ID: mdl-28646906

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Fosforilação Oxidativa / Complexo I de Transporte de Elétrons / Células-Tronco Mesenquimais / Fibroblastos / Mitocôndrias / NADH Desidrogenase Limite: Animals / Humans Idioma: En Revista: Stem Cell Res Ther Ano de publicação: 2017 Tipo de documento: Article País de afiliação: Alemanha País de publicação: Reino Unido

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Fosforilação Oxidativa / Complexo I de Transporte de Elétrons / Células-Tronco Mesenquimais / Fibroblastos / Mitocôndrias / NADH Desidrogenase Limite: Animals / Humans Idioma: En Revista: Stem Cell Res Ther Ano de publicação: 2017 Tipo de documento: Article País de afiliação: Alemanha País de publicação: Reino Unido