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Absence of full-length dystrophin impairs normal maturation and contraction of cardiomyocytes derived from human-induced pluripotent stem cells.
Pioner, J Manuel; Guan, Xuan; Klaiman, Jordan M; Racca, Alice W; Pabon, Lil; Muskheli, Veronica; Macadangdang, Jesse; Ferrantini, Cecilia; Hoopmann, Michael R; Moritz, Robert L; Kim, Deok-Ho; Tesi, Chiara; Poggesi, Corrado; Murry, Charles E; Childers, Martin K; Mack, David L; Regnier, Michael.
Afiliação
  • Pioner JM; Experimental and Clinical Medicine, Div. of Physiology, University of Florence, Florence, Italy.
  • Guan X; Bioengineering, University of Washington, Seattle, WA, USA.
  • Klaiman JM; Bioengineering, University of Washington, Seattle, WA, USA.
  • Racca AW; School of Biosciences, University of Kent, Canterbury, UK.
  • Pabon L; Pathology, University of Washington, Seattle, WA, USA.
  • Muskheli V; Center for Cardiovascular Biology, University of Washington, Seattle, WA, USA.
  • Macadangdang J; Institute for Stem Cell and Regenerative Medicine, University of Washington, Seattle, USA.
  • Ferrantini C; Center for Cardiovascular Biology, University of Washington, Seattle, WA, USA.
  • Hoopmann MR; Bioengineering, University of Washington, Seattle, WA, USA.
  • Moritz RL; Experimental and Clinical Medicine, Div. of Physiology, University of Florence, Florence, Italy.
  • Kim DH; Institute for Systems Biology, Seattle, Washington, USA.
  • Tesi C; Institute for Systems Biology, Seattle, Washington, USA.
  • Poggesi C; Bioengineering, University of Washington, Seattle, WA, USA.
  • Murry CE; Institute for Stem Cell and Regenerative Medicine, University of Washington, Seattle, USA.
  • Childers MK; Experimental and Clinical Medicine, Div. of Physiology, University of Florence, Florence, Italy.
  • Mack DL; Experimental and Clinical Medicine, Div. of Physiology, University of Florence, Florence, Italy.
  • Regnier M; Bioengineering, University of Washington, Seattle, WA, USA.
Cardiovasc Res ; 116(2): 368-382, 2020 02 01.
Article em En | MEDLINE | ID: mdl-31049579

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Diferenciação Celular / Distrofina / Distrofia Muscular de Duchenne / Miócitos Cardíacos / Células-Tronco Pluripotentes Induzidas / Contração Miocárdica / Cardiomiopatias / Miofibrilas Tipo de estudo: Observational_studies / Risk_factors_studies Limite: Humans Idioma: En Revista: Cardiovasc Res Ano de publicação: 2020 Tipo de documento: Article País de afiliação: Itália País de publicação: Reino Unido

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Diferenciação Celular / Distrofina / Distrofia Muscular de Duchenne / Miócitos Cardíacos / Células-Tronco Pluripotentes Induzidas / Contração Miocárdica / Cardiomiopatias / Miofibrilas Tipo de estudo: Observational_studies / Risk_factors_studies Limite: Humans Idioma: En Revista: Cardiovasc Res Ano de publicação: 2020 Tipo de documento: Article País de afiliação: Itália País de publicação: Reino Unido