Your browser doesn't support javascript.
loading
Pure Bladder Malignant Rhabdoid Tumor Successfully Treated With Partial Cystectomy, Radiation, and Chemotherapy: A Case Report and Review of the Literature.
Assadi, Akram; Alzubaidi, Ahmad; Lesmana, Harry; Brennan, Rachel C; Saad, Ali; Ortiz-Hernández, Vanessa; Gleason, Joseph M.
Afiliação
  • Assadi A; Departments of Urology.
  • Alzubaidi A; Division of Pediatric Urology, Le Bonheur Children's Hospital.
  • Lesmana H; Departments of Surgery.
  • Brennan RC; Departments of Urology.
  • Saad A; Hematology.
  • Ortiz-Hernández V; Oncology, St. Jude Children's Research Hospital.
  • Gleason JM; Oncology, St. Jude Children's Research Hospital.
J Pediatr Hematol Oncol ; 43(8): e1214-e1216, 2021 Nov 01.
Article em En | MEDLINE | ID: mdl-33031160
ABSTRACT

BACKGROUND:

Extracranial pure malignant rhabdoid tumors (MRT) are aggressive tumors that carry a poor prognosis. Bladder MRTs are very rare and only 8 cases have been reported previously. OBSERVATION We present a case of a child with bladder MRT. Despite the aggressive nature of the bladder tumor, it was successfully treated with bladder-sparing surgery, adjuvant radiotherapy, and chemotherapy.

CONCLUSIONS:

Our case, and review of 8 previously reported cases, suggests that bladder MRT seems to behave less aggressively when compared with other extracranial MRTs, and bladder preserving surgery should be considered when feasible.
Assuntos

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Neoplasias da Bexiga Urinária / Cistectomia / Quimioterapia Adjuvante / Tumor Rabdoide / Radioterapia Adjuvante Tipo de estudo: Prognostic_studies Limite: Child, preschool / Humans / Male Idioma: En Revista: J Pediatr Hematol Oncol Assunto da revista: HEMATOLOGIA / NEOPLASIAS / PEDIATRIA Ano de publicação: 2021 Tipo de documento: Article

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Neoplasias da Bexiga Urinária / Cistectomia / Quimioterapia Adjuvante / Tumor Rabdoide / Radioterapia Adjuvante Tipo de estudo: Prognostic_studies Limite: Child, preschool / Humans / Male Idioma: En Revista: J Pediatr Hematol Oncol Assunto da revista: HEMATOLOGIA / NEOPLASIAS / PEDIATRIA Ano de publicação: 2021 Tipo de documento: Article