Efficacy of intravenous immunoglobulin in shrinking lung syndrome associated with mixed connective tissue disease: a case report.
Clin Exp Rheumatol
; 40 Suppl 134(5): 116-117, 2022 May.
Article
em En
| MEDLINE
| ID: mdl-35084319
ABSTRACT
Shrinking lung syndrome is a rare manifestation of connective tissue diseases, namely systemic lupus erythematosus. It is characterised by reduced lung volumes and extra-pulmonary restrictive ventilatory pattern with good response to high-dose glucocorticoids alone or in combination with a second immunosuppressive agent. Here, we describe a case associated with mixed connective tissue disease and effectively treated with intravenous immunoglobulin.
Texto completo:
1
Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Pneumopatias
/
Lúpus Eritematoso Sistêmico
/
Doença Mista do Tecido Conjuntivo
/
Doenças Musculares
Tipo de estudo:
Diagnostic_studies
/
Etiology_studies
/
Risk_factors_studies
Limite:
Humans
Idioma:
En
Revista:
Clin Exp Rheumatol
Ano de publicação:
2022
Tipo de documento:
Article
País de afiliação:
Portugal
País de publicação:
IT
/
ITALIA
/
ITALY
/
ITÁLIA