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Physical training and high-protein diet improved muscle strength, parent-reported fatigue, and physical quality of life in children with Pompe disease.
Scheffers, L E; Somers, O C; Dulfer, K; Dieleman, G C; Walet, S; van der Giessen, L J; van der Ploeg, A T; van den Hout, J M P; van den Berg, L E.
Afiliação
  • Scheffers LE; Department of pediatrics, Center for Lysosomal and Metabolic Diseases, Erasmus MC University Medical Center, Rotterdam, The Netherlands.
  • Somers OC; Respiratory Medicine and Allergology, Department of Pediatrics, Erasmus MC University Medical Center-Sophia Children's Hospital, Rotterdam, The Netherlands.
  • Dulfer K; Department of Pediatric Gastroenterology, Erasmus MC University Medical Center-Sophia Children's Hospital, Rotterdam, The Netherlands.
  • Dieleman GC; Department of Pediatric Cardiology, Erasmus MC University Medical Center-Sophia Children's Hospital, Rotterdam, The Netherlands.
  • Walet S; Department of pediatrics, Center for Lysosomal and Metabolic Diseases, Erasmus MC University Medical Center, Rotterdam, The Netherlands.
  • van der Giessen LJ; Intensive Care and Department of Pediatric Surgery, Erasmus MC University Medical Center-Sophia Children's Hospital, Rotterdam, The Netherlands.
  • van der Ploeg AT; Department of Child and Adolescent Psychiatry/Psychology, Erasmus MC University Medical Center-Sophia Children's Hospital, Rotterdam, The Netherlands.
  • van den Hout JMP; Division of Dietetics, Department of Internal Medicine, Erasmus MC University Medical Center, Rotterdam, The Netherlands.
  • van den Berg LE; Department of Pediatric Physiotherapy, Erasmus MC University Medical Center, Rotterdam, The Netherlands.
J Inherit Metab Dis ; 46(4): 605-617, 2023 07.
Article em En | MEDLINE | ID: mdl-37002894

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Doença de Depósito de Glicogênio Tipo II / Dieta Rica em Proteínas Tipo de estudo: Clinical_trials / Prognostic_studies Aspecto: Patient_preference Limite: Adolescent / Child / Humans Idioma: En Revista: J Inherit Metab Dis Ano de publicação: 2023 Tipo de documento: Article País de afiliação: Holanda País de publicação: Estados Unidos

Texto completo: 1 Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Doença de Depósito de Glicogênio Tipo II / Dieta Rica em Proteínas Tipo de estudo: Clinical_trials / Prognostic_studies Aspecto: Patient_preference Limite: Adolescent / Child / Humans Idioma: En Revista: J Inherit Metab Dis Ano de publicação: 2023 Tipo de documento: Article País de afiliação: Holanda País de publicação: Estados Unidos