Two challenging cases of anti-MDA-5 dermatomyositis with rapidly progressive interstitial lung disease.
Oxf Med Case Reports
; 2024(6): omae061, 2024 Jun.
Article
em En
| MEDLINE
| ID: mdl-38860011
ABSTRACT
Anti-MDA-5 dermatomyositis (DM) is a subtype of idiopathic inflammatory myopathy, commonly presenting as clinically amyopathic dermatomyositis. It is associated with rapidly progressive interstitial lung disease and a poor prognosis. Here, we present two cases of anti-MDA-5 DM and discuss the challenges associated with timely diagnosis, and the importance of early and aggressive treatment.
Texto completo:
1
Coleções:
01-internacional
Base de dados:
MEDLINE
Idioma:
En
Revista:
Oxf Med Case Reports
Ano de publicação:
2024
Tipo de documento:
Article
País de publicação:
Reino Unido