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[Acute hemolysis and liver cirrhosis as leading symptoms of Wilson's disease in childhood]. / Akute Hämolyse und Leberzirrhose als führende Symptome eines Morbus Wilson im Kindesalter.
Klin Padiatr ; 195(5): 355-7, 1983.
Article em De | MEDLINE | ID: mdl-6632716
ABSTRACT
Acute hemolytic anemia and the development of liver cirrhosis with ascites 3 month thereafter suggested Wilson's disease in a 12 years old child, which was confirmed by inappropriate copper metabolism. In addition, neurological symptoms and renal tubular insufficiency characterized the early stage of the disease.
Assuntos
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Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Degeneração Hepatolenticular / Anemia Hemolítica / Cirrose Hepática Tipo de estudo: Diagnostic_studies / Etiology_studies Limite: Child / Humans / Male Idioma: De Revista: Klin Padiatr Ano de publicação: 1983 Tipo de documento: Article
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Coleções: 01-internacional Base de dados: MEDLINE Assunto principal: Degeneração Hepatolenticular / Anemia Hemolítica / Cirrose Hepática Tipo de estudo: Diagnostic_studies / Etiology_studies Limite: Child / Humans / Male Idioma: De Revista: Klin Padiatr Ano de publicação: 1983 Tipo de documento: Article