Oral manifestations in glycogen storage disease type 1b.
J Oral Pathol Med
; 24(3): 136-9, 1995 Mar.
Article
em En
| MEDLINE
| ID: mdl-7776266
ABSTRACT
Glycogen storage disease type 1b is a rare metabolic disorder which affects the transport system of glucose-6-phosphatase metabolism. As a result, hepatomegaly, failure to thrive, renal dysfunction and recurrent infections occur in affected patients. In this paper, the oral complications in three children with glycogen storage disease type 1b are discussed. Oral ulcers were a common finding, probably due to severe neutropenia and impaired neutrophil migration which characterises the onset of this rare disorder.
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Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Doença de Depósito de Glicogênio Tipo I
/
Doenças da Boca
Limite:
Child, preschool
/
Female
/
Humans
/
Male
/
Newborn
Idioma:
En
Revista:
J Oral Pathol Med
Assunto da revista:
ODONTOLOGIA
/
PATOLOGIA
Ano de publicação:
1995
Tipo de documento:
Article
País de afiliação:
Grécia