[POEMS syndrome with primary adrenocortical insufficiency]. / Syndrome de POEMS avec insuffisance surrénalienne primaire.
Presse Med
; 27(1): 15-7, 1998 Jan 10.
Article
em Fr
| MEDLINE
| ID: mdl-9767755
ABSTRACT
BACKGROUND:
POEMS syndrome is a multisystem disorder. It usually presents as severe polyneuropathy and monoclonal gammapathy associated with endocrinopathies, organomegaly, skin hyperpigmentation. CASE REPORT A patient with POEMS syndrome developed primary adrenocortical deficiency revelated by asthenia and hyperpigmentation. Hydrocortisone replacement therapy produced a rapidly beneficial effect on asthenia and hyperpigmentation.DISCUSSION:
Although asthenia and skin pigmentation are common in POEMS syndrome, adrenocortical deficiency is seldom reported. This endocrinopathy might be underestimated in POEMS patients. We suggest systematic screening with a rapid ACTH test in all POEMS patients in order to detect underlying adrenal deficiency.
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Coleções:
01-internacional
Base de dados:
MEDLINE
Assunto principal:
Hidrocortisona
/
Síndrome POEMS
/
Insuficiência Adrenal
Tipo de estudo:
Diagnostic_studies
Limite:
Humans
/
Male
/
Middle aged
Idioma:
Fr
Revista:
Presse Med
Ano de publicação:
1998
Tipo de documento:
Article