Askin Tumor: Malignant Round Cell Tumor in Thoraco-pulmonary Region in a Young Male Child.

ABSTRACT

Askin's tumor is a rare tumor arising from the chest wall. It is known to be a subset of Ewing’s sarcoma histologically presenting as a small round blue cells. It is a highly malignant tumor with poor prognosis. 17-year-old teenager visited in our department with complaints of chest pain and swelling. Chest skiagram revealed a homogenous radio opacity in the right mid/ lower hemithorax. NECT and CECT thorax was done and was suggestive of two lesions in chest. One large lytic lesion involving the right lower ribs (6th, 7th) associated with large heterogeneous soft tissue mass on medial side. The other causing destruction of body of D8 vertebra associated with a paravertebral soft tissue mass. The diagnosis was further confirmed by biopsy of 6th rib which was suggestive of small round cell tumor.