Endoscopic Decompression for Optic Neuropathy in McCune-Albright Syndrome
Journal of Korean Neurosurgical Society
; : 281-283, 2014.
Artigo
em Inglês
| WPRIM (Pacífico Ocidental)
| ID: wpr-140380
Biblioteca responsável:
WPRO
ABSTRACT
McCune-Albright syndrome (MAS) is characterized by a triad of poly/monostotic fibrous dysplasia, cafe-au-lait macules and hyperfunctioning endocrinopathies including human growth hormone excess. Acromegaly as a manifestation of endocrine hyperfunction with MAS is uncommon. Surgical excision may be challenging due to the associated severe fibrous dysplasia of the skull base. Through the endoscopic procedures, we treated a case of MAS presenting with compressive optic neuropathy due to fibrous dysplasia and acromegaly caused by growth hormone secreting pituitary adenoma. We reviewed the literature on GH excess in MAS to highlight its surgical and medical challenges.
Texto completo:
Disponível
Base de dados:
WPRIM (Pacífico Ocidental)
Assunto principal:
Neoplasias Hipofisárias
/
Acromegalia
/
Hormônio do Crescimento
/
Doenças do Nervo Óptico
/
Base do Crânio
/
Hormônio do Crescimento Humano
/
Descompressão
/
Displasia Fibrosa Poliostótica
Idioma:
Inglês
Revista:
Journal of Korean Neurosurgical Society
Ano de publicação:
2014
Tipo de documento:
Artigo