Undifferentiated Carcinoma Arising in a Choledochal Cyst: A Case Report
Korean Journal of Pathology
; : 461-465, 2006.
Article
em En
| WPRIM
| ID: wpr-157918
Biblioteca responsável:
WPRO
ABSTRACT
An association between choledochal cyst and carcinoma is well established. Here, we report an extremely rare case of undifferentiated carcinoma exhibiting extensive sarcomatous features arising in a choledochal cyst. The patient in our case had a radiologically confirmed choledochal cyst and anomalous pancreaticobiliary ductal union, and mild wall thickening in the cyst was observed on endoscopic retrograde cholangiopancreatography. The patient underwent common bile duct excision and cholecystectomy. In the choledochal cyst, a nodule measuring 1.5x1 cm was detected. The lesion was composed of atypical, spindle-shaped and large, round pleomorphic tumor cells simulating sarcoma. Neither glandular nor squamous differentiation was observed. These cells were immunoreactive for both vimentin and cytokeratin by immunohistochemistry. These histologic and immunohistochemical findings were consistent with undifferentiated carcinoma, spindle and giant cell type, according to the WHO classification.
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Texto completo:
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Base de dados:
WPRIM
Assunto principal:
Sarcoma
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Vimentina
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Imuno-Histoquímica
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Colecistectomia
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Carcinoma
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Cisto do Colédoco
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Células Gigantes
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Colangiopancreatografia Retrógrada Endoscópica
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Classificação
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Ducto Colédoco
Limite:
Humans
Idioma:
En
Revista:
Korean Journal of Pathology
Ano de publicação:
2006
Tipo de documento:
Article