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A Case of Acroosteolysis in Primary Hypertrophic Osteoarthropathy
Article em Ko | WPRIM | ID: wpr-171508
Biblioteca responsável: WPRO
ABSTRACT
Primary hypertrophic osteoarthropathy or pachydermoperiostosis is a rare hereditary disorder characterized by digital clubbing, pachydermia and periostosis. Its precise incidence and prevalence is still unknown due to the lack of controlled data. It occurs without any underlying causes and usually has a chronic course. Life expectancy may be of normal standards, but many patients develop multiple functional and cosmetic complications. So, it is important to diagnose this disease at an early stage and to treat the symptomat for the quality of life. We report a case of primary hypertrophic osteoarthropathy in a 68-year-old male with clinical features such as digital clubbing and pachydermia, radiographic findings of acroosteolysis and periosteal new bone formation.
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Texto completo: 1 Base de dados: WPRIM Assunto principal: Osteoartropatia Hipertrófica Primária / Qualidade de Vida / Incidência / Expectativa de Vida / Acro-Osteólise Tipo de estudo: Guideline / Incidence_studies / Prognostic_studies Aspecto: Patient_preference Limite: Aged / Humans / Male Idioma: Ko Revista: Journal of Rheumatic Diseases Ano de publicação: 2013 Tipo de documento: Article
Texto completo: 1 Base de dados: WPRIM Assunto principal: Osteoartropatia Hipertrófica Primária / Qualidade de Vida / Incidência / Expectativa de Vida / Acro-Osteólise Tipo de estudo: Guideline / Incidence_studies / Prognostic_studies Aspecto: Patient_preference Limite: Aged / Humans / Male Idioma: Ko Revista: Journal of Rheumatic Diseases Ano de publicação: 2013 Tipo de documento: Article