Multiple Aortic Operations in Loeys-Dietz Syndrome: Report of 2 Cases
The Korean Journal of Thoracic and Cardiovascular Surgery
; : 536-540, 2014.
Article
em En
| WPRIM
| ID: wpr-187576
Biblioteca responsável:
WPRO
ABSTRACT
Due to its low prevalence and because there is lack of awareness about it, Loeys-Dietz syndrome is often mis-diagnosed as Marfan syndrome, which has similar skeletal abnormalities and aortic pathology. However, the differential diagnosis between these two connective tissue diseases is critical because they correspond to different surgical indications and surgical decision-making. We report two cases of successful thoracoabdominal aortic replacement in patients with previously undiagnosed Loeys-Dietz syndrome.
Palavras-chave
Texto completo:
1
Base de dados:
WPRIM
Assunto principal:
Aneurisma Aórtico
/
Patologia
/
Prevalência
/
Doenças do Tecido Conjuntivo
/
Diagnóstico Diferencial
/
Síndrome de Loeys-Dietz
/
Síndrome de Marfan
Tipo de estudo:
Diagnostic_studies
/
Prevalence_studies
Limite:
Humans
Idioma:
En
Revista:
The Korean Journal of Thoracic and Cardiovascular Surgery
Ano de publicação:
2014
Tipo de documento:
Article