Extramammary Paget's Disease Involving the Scrotum and Umbilicus

ABSTRACT

Extramammary Paget's disease (EMPD) is a rare intraepithelial adenocarcinoma. To date, about 200 cases of EMPD have been reported since the first report in 1889. There has been only one case of EMPD involving the umbilicus, in a patient with prostatic carcinoma. This is the first report of EMPD occurring concurrently in the scrotum and umbilicus. The patient had recurrent, eczematous, and pruritic lesions of the left scrotum and umbilicus 2 years previously. Biopsy and surgical resection were performed and EMPD was diagnosed. There was no evidence of recurrence at 34 months after surgery.