A Case of Mantle Cell Lymphoma Presenting as Multiple Lymphomatous Polyposis Involving Skeletal Muscles / 대한소화기내시경학회지
Korean Journal of Gastrointestinal Endoscopy
; : 15-20, 2003.
Article
em Ko
| WPRIM
| ID: wpr-211181
Biblioteca responsável:
WPRO
ABSTRACT
Multiple lymphomatous polyposis (MLP) is an uncommon type of primary non-Hodgkin's gastrointestinal B cell-lymphoma characterized by the presence of multiple lymphomatous polyps along the gastrointestinal tract. Unlike MALT-lymphoma, MLP has a strong tendency for histologically monomorphic character, extra-digestive localization, rare lymphoepithelial lesion and poor prognosis. The malignant cells of MLP share morphological, immunohistologic and cytogenetic similarities with cells of node-based mantle cell lymphoma. We report a case of mantle cell lymphoma presenting with MLP involving various segments of the gastrointestinal tract, skeletal muscles of the right thigh and bone marrow observed in a 71-year-old woman who complained of lower abdominal pain and a palpable right thigh mass.
Palavras-chave
Texto completo:
1
Base de dados:
WPRIM
Assunto principal:
Pólipos
/
Prognóstico
/
Coxa da Perna
/
Medula Óssea
/
Dor Abdominal
/
Músculo Esquelético
/
Linfoma de Célula do Manto
/
Citogenética
/
Trato Gastrointestinal
Tipo de estudo:
Prognostic_studies
Limite:
Aged
/
Female
/
Humans
Idioma:
Ko
Revista:
Korean Journal of Gastrointestinal Endoscopy
Ano de publicação:
2003
Tipo de documento:
Article