A Case of Bilateral Adrenal Myelolipomas with Congenital Adrenal Hyperplasia / 대한내과학회지
Korean Journal of Medicine
; : 340-345, 2015.
Article
em Ko
| WPRIM
| ID: wpr-216643
Biblioteca responsável:
WPRO
ABSTRACT
Adrenal myelolipoma (AML) is a rare, usually benign, and nonfunctioning tumor. About 7-15% of adrenal incidentalomas are AMLs, composed of normal hematopoietic elements and mature adipose tissue. AML is usually unilateral and < 4 cm. It is often discovered incidentally on abdominal computed tomography or magnetic resonance imaging. It is related to a chronic increase in adrenocorticotropic hormone, such as that observed in patients with congenital adrenal hyperplasia, Cushing disease, Conn's syndrome, and pheochromocytoma. Here, we report a 28-year-old man diagnosed with non-salt-losing congenital adrenal hyperplasia with huge bilateral AMLs and a literature review.
Palavras-chave
Texto completo:
1
Base de dados:
WPRIM
Assunto principal:
Feocromocitoma
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Imageamento por Ressonância Magnética
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Tecido Adiposo
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Mielolipoma
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Hiperplasia Suprarrenal Congênita
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Hormônio Adrenocorticotrópico
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Hipersecreção Hipofisária de ACTH
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Hiperaldosteronismo
Limite:
Adult
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Humans
Idioma:
Ko
Revista:
Korean Journal of Medicine
Ano de publicação:
2015
Tipo de documento:
Article