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Maffucci's Syndrome Associated with Chondrosarcoma and Aneurysm: Case Report
Article em En | WPRIM | ID: wpr-30225
Biblioteca responsável: WPRO
ABSTRACT
Maffucci syndrome is a rare congenital non-inherited condition characterized by multiple enchondromas and cutaneous hemangiomas. It is associated with increased risk of malignancy, including chondrosarcomas, and because of generalized mesodermal dysplasia, aneurysms can develop. We present a case of Maffucci syndrome associated with intracranial chondrosarcoma and aneurysm.
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Texto completo: 1 Base de dados: WPRIM Assunto principal: Aneurisma Intracraniano / Condroma / Condrossarcoma / Encondromatose / Hemangioma / Aneurisma / Mesoderma Idioma: En Revista: Journal of the Korean Radiological Society Ano de publicação: 2002 Tipo de documento: Article
Texto completo: 1 Base de dados: WPRIM Assunto principal: Aneurisma Intracraniano / Condroma / Condrossarcoma / Encondromatose / Hemangioma / Aneurisma / Mesoderma Idioma: En Revista: Journal of the Korean Radiological Society Ano de publicação: 2002 Tipo de documento: Article