A Pediatric Case of Inflammatory Bowel Disease with Renal Amyloidosis
Childhood Kidney Diseases
; : 81-85, 2018.
Article
em En
| WPRIM
| ID: wpr-739193
Biblioteca responsável:
WPRO
ABSTRACT
Amyloidosis is a rare disease that results from the deposition of extracellular protein in various body tissues, causing progressive organ dysfunction. Secondary renal amyloidosis is a rare but serious complication of chronic inflammatory bowel disease, particularly in patients with Crohn's disease or ulcerative colitis. We report a case of secondary renal amyloidosis in a pediatric patient who reported a 16-year history of “very early onset inflammatory bowel disease”. Intensive treatment including repeated infliximab infusions improved clinical parameters of inflammatory bowel disease, although renal dysfunction showed progression. Amyloidosis should be considered in patients with IBD, particularly if they suffered disease progression.
Palavras-chave
Texto completo:
1
Base de dados:
WPRIM
Assunto principal:
Doenças Inflamatórias Intestinais
/
Colite Ulcerativa
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Doença de Crohn
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Progressão da Doença
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Doenças Raras
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Infliximab
/
Amiloidose
Limite:
Humans
Idioma:
En
Revista:
Childhood Kidney Diseases
Ano de publicação:
2018
Tipo de documento:
Article