Two Cases of Malignant Lymphomas in Children with Selective IgA and IgG Subclass Deficiency / 대한소아혈액종양학회지
Korean Journal of Pediatric Hematology-Oncology
; : 253-259, 2004.
Article
em Ko
| WPRIM
| ID: wpr-74193
Biblioteca responsável:
WPRO
ABSTRACT
Selective IgA deficiency is one of the most common primary immunodeficiency. Some patients with IgA deficiency also have deficits in one or more immunoglobulin G subclasses. It has been estimated that up to 25% of patients with certain primary immunodeficiencies will develop tumors, primarily B-cell lymphomas during their lifetime. We hereby present 2 cases of malignant lymphomas, one diffuse large cell lymphoma and another mixed cellularity Hodgkin's disease, respectively, which developed in patients with selective IgA and IgG subclass deficiency.
Palavras-chave
Texto completo:
1
Base de dados:
WPRIM
Assunto principal:
Linfoma não Hodgkin
/
Imunoglobulina A
/
Imunoglobulina G
/
Doença de Hodgkin
/
Linfoma de Células B
/
Linfoma Difuso de Grandes Células B
/
Deficiência de IgA
/
Linfoma
Limite:
Child
/
Humans
Idioma:
Ko
Revista:
Korean Journal of Pediatric Hematology-Oncology
Ano de publicação:
2004
Tipo de documento:
Article