Non-IgG4-Related Fibrosclerosing Periaortitis with Multisystemic Involvement / 대한내과학회지
Korean Journal of Medicine
; : 749-754, 2014.
Article
em Ko
| WPRIM
| ID: wpr-85489
Biblioteca responsável:
WPRO
ABSTRACT
Fibrosclerosing periaortitis is a rare condition that refers to a spectrum of idiopathic diseases characterized by a fibroinflammatory reaction that extends from the adventitia of the aorta into the surrounding structures. It can be present in either IgG4-related or non-IgG4-related fibrosclerosing periaortitis. IgG4-related fibrosclerosing periaortitis could be associated with concomitant multi-organ involvement. However, non-IgG4-related fibrosclerosing periaortitis has rarely been associated with systemic manifestations. Here, we report a 76-year-old female with non-IgG4-related fibrosclerosing periaortitis, who developed pancytopenia, pleural effusion and ascites, which improved after high dose steroid treatment.
Palavras-chave
Texto completo:
1
Base de dados:
WPRIM
Assunto principal:
Aorta
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Pancitopenia
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Derrame Pleural
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Ascite
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Fibrose Retroperitoneal
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Imunoglobulina G
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Túnica Adventícia
Limite:
Aged
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Female
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Humans
Idioma:
Ko
Revista:
Korean Journal of Medicine
Ano de publicação:
2014
Tipo de documento:
Article