Malignant Fibrous Histiocytoma with Type I Neurofibromatosis
Journal of the Korean Surgical Society
; : 167-170, 2004.
Article
em Ko
| WPRIM
| ID: wpr-92214
Biblioteca responsável:
WPRO
ABSTRACT
Type I neurofibromatosis is an autosomal dominant disorder that occurs in 1 of 3, 000 births. It is characterized by multiple cutaneous neurofibromas, cafe-au-lait spots of the skin. Patients with neurofibromatosis are at increased risk of developing malignancies, particularly neural crest and other non-neural crest neoplasms. The term `malignant fibrous histiocytoma' was first introduced in 1963 to refer to a group of soft tissue tumors characterized by a storiform or cartwheel like growth pattern. Malignant fibrous histiocytomas are the most common type of soft tissue sarcoma that occurs in late adult life. Herein, our recent experienced a case of a malignant fibrous histiocytoma in a 28 year-old female with type I neurofibromatosis is reported, with a review of the literature.
Palavras-chave
Texto completo:
1
Base de dados:
WPRIM
Assunto principal:
Sarcoma
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Pele
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Neurofibromatose 1
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Neurofibromatoses
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Manchas Café com Leite
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Parto
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Histiocitoma Fibroso Maligno
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Crista Neural
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Neurofibroma
Limite:
Adult
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Female
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Humans
Idioma:
Ko
Revista:
Journal of the Korean Surgical Society
Ano de publicação:
2004
Tipo de documento:
Article